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Essential Biochemistry - Lipid Metabolism (Section 11 - No. 45)

Which enzyme is defective in Tay-Sachs disease?
Hexosaminidase A
Sphingomyelinase
Glucocerebrosidase
β-galactosidase

Explanation

Tay-Sachs disease is caused by a deficiency of hexosaminidase A.

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